Sclerodermia, Diffuse

Muscular Atrophy and Sclerodermia

Best practices in scleroderma: an analysis of practice variability in SSc centres within the Canadian Scleroderma Research Group (CSRG).

OBJECTIVES There is currently no consensus on best practice in systemic sclerosis (SSc). To determine if variability in treatment and investigations exists, practices among Canadian Sclerodermia Research Group (CSRG) centres were compared. METHODS Prospective clinical and demographic data from adult SSc patients are collected annually from 15 CSRG treatment centres. Laboratory parameters, sel...

DIFFUSE REFLECTANCE MEASUREMENTS FROM DIFFERENT SURFACES

Relative diffuse reflection measurements from the original and ground surfaces using a He-Ne laser are reported. The intensity measurements for the metallic, transparent dielectric, matte plastic surfaces and colored papers are presented. Our results indicate that among metallic surfaces tested, aluminum has the highest diffuse reflectance; while the original stainless steel surface shows the l...

Congenital diffuse Melanosis in a father and two sons

Congenital diffuse Melanosis is one of the rarest clinical manifestations of hereditary universal Melanosis and only few cases have been reported all over the world. The presented case is a 54-year-old man who presented to us complaining of erythematous annular lesions on his face and neck since 8 months ago. Diffuse pigmentation of his skin took our attention. According to the patient, d...

Manifestation of connective tissue diseases (CTD) in pediatrics patients with autoimmune hepatitis (AIH)

Background Autoimmune hepatitis (AIH) is a progressive inflammatory fribrosing disease of the liver of unknown etiology, which in its normal progress leads to cirrhosis. It is characterized by the increase in aminotranferases and hypergammaglobulinemia, and the presence of nonorgan and specific liver autoantibodies in serum, which allow for its classification. Two subtypes are differentiated: T...